Question

hepatolenticular degeneration is an inherited metabolic disorder in which the patient is deficient in the carrier protein ceruloplasmin, resulting in accumulation which of the following in the basal ganglia?
sphingomyelin
phenylalanine
copper
iron

Explanation:

Hepatolenticular Degeneration (Wilson's disease) is a disorder where there's a deficiency of ceruloplasmin, a protein that transports copper. Without enough ceruloplasmin, copper can't be properly excreted and accumulates, including in the basal ganglia. Sphingomyelin accumulation is related to Niemann - Pick disease, phenylalanine accumulation to phenylketonuria, and iron accumulation to hemochromatosis, so copper is the correct answer.

Answer:

Copper (the option with "Copper" as the text)